A rare presentation of Rapunzel syndrome with multiple small bowel intussusceptions

oleh: Kyoung Jeen Min, Hann Tchah, Seong Min Kim, Jea Yeon Choi

Format: Article
Diterbitkan: Korean Society of Pediatric Emergency Medicine 2019-06-01

Deskripsi

Rapunzel syndrome is caused by gastric trichobezoar with extended tail and small bowel obstruction. Patients with gastric trichobezoar can be asymptomatic until the bezoar increases in size. We report a case of a girl who visited the emergency department with abdominal pain. She was finally diagnosed with Rapunzel syndrome that causes multiple small bowel intussusceptions associated with trichophagia. Surgery was needed to reduce the multiple intussusceptions, and to remove the large trichobezoar. This case highlights to consider the possibility of Rapunzel syndrome when diagnosing the main cause of intussusceptions.