Biopsy-Proven Lymphocytic Myocarditis With Heart Failure in a Middle-Aged Female Patient With Mixed Connective Tissue Disease

oleh: Stefano Figliozzi, MD, Stefania Rizzo, MD, Chun-Yan Cheng, MD, PhD, Sabino Iliceto, MD, Cristina Basso, MD, PhD, Alida L.P. Caforio, MD, PhD, Renzo Marcolongo, MD

Format: Article
Diterbitkan: Elsevier 2019-08-01

Deskripsi

A 56-year-old woman with mixed connective tissue disease, who was on maintenance immunosuppression, developed asymptomatic left ventricular dysfunction, ventricular arrhythmia, and high troponin I. Heart catheterization showed normal coronaries and biopsy-proven, virus-negative lymphocytic myocarditis. A biopsy-guided immunosuppression upgrade effectively treated autoimmune myocarditis, which resulted in ventricular function recovery, resolution of arrhythmia, and of troponin release. (Level of Difficulty: Advanced.)