Case Report: Partial nephrectomy in primary renal sarcoma presenting as Wunderlich syndrome; a rare tumour with rare presentation managed atypically [version 1; peer review: 1 approved, 2 approved with reservations]
oleh: Ramanitharan Manikandan, Ketan Mehra, Lalgudi Narayanan Dorairajan, Rajesh Nachiappa Ganesh, Sreerag K. Sreenivasan, Rajeev Kumar
| Format: | Article |
|---|---|
| Diterbitkan: | F1000 Research Ltd 2019-04-01 |
Deskripsi
Spontaneous retroperitoneal haemorrhage also called Wunderlich Syndrome (WS) may be caused by various aetiologies. One of the most common causes is renal tumour. Renal sarcoma is a rare cause of WS, and renal sarcoma in itself is a rare entity. In the era of nephron-sparing surgery, optimum management of primary renal sarcoma remains a dilemma as there are limited number of cases available in the literature. Nevertheless, radical nephrectomy remains the recommended treatment, keeping in mind the aggressiveness of the tumour. We report a case of primary undifferentiated renal sarcoma, which presented as WS, and which was managed by partial nephrectomy.