Unilateral lateral mass hypertrophy: An extremely rare congenital anomaly of Atlas

oleh: Kuntal Kanti Das, Anant Mehrotra, Rabi Narayan Sahu, Arun Kumar Srivastava, Awadhesh Kumar Jaiswal, Sanjay Behari

Format: Article
Diterbitkan: Wolters Kluwer Medknow Publications 2013-01-01

Deskripsi

A wide variety of congenital anomalies are observed around the craniovertebral junctional area. However, hypertrophied unilateral lateral mass of atlas in association with chiari-1 malformation leading to myelopathy is extremely uncommon. Herein we report a case of 28-year-old female who presented to us with a high cervical compressive myelopathy. Imaging revealed bony hypertrophy involving right sided C1 lateral mass along with chiari malformation-type 1. She underwent transoral as well as posterior decompression followed by occipito-cervical fusion. The authors discuss their case in light of other such reported cases and present a review of the literature.