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Bloch Sulzberger syndrome (Incontinentia pigmenti): A rare case report with dental defects
oleh: Yaga Uday Shankar, Nikhat Fatima, Menji Ashwini Kumar, Kesary Sathya Prakash
Format: | Article |
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Diterbitkan: | Wolters Kluwer Medknow Publications 2015-01-01 |
Deskripsi
Incontinentia Pigmenti (IP) is a multisystem genodermatosis characterized by cutaneous, neurologic, ophthalmologic, and dental abnormalities. This article reports the clinical features and management of a 4-year-old girl diagnosed with IP.