Bloch Sulzberger syndrome (Incontinentia pigmenti): A rare case report with dental defects

oleh: Yaga Uday Shankar, Nikhat Fatima, Menji Ashwini Kumar, Kesary Sathya Prakash

Format: Article
Diterbitkan: Wolters Kluwer Medknow Publications 2015-01-01

Deskripsi

Incontinentia Pigmenti (IP) is a multisystem genodermatosis characterized by cutaneous, neurologic, ophthalmologic, and dental abnormalities. This article reports the clinical features and management of a 4-year-old girl diagnosed with IP.