Cerebral Amyloid Angiopathy Related Inflammation With Prominent Meningeal Involvement. A Report of 2 Cases

oleh: Agnès Aghetti, Agnès Aghetti, Damien Sène, Damien Sène, Marc Polivka, Natalia Shor, Sarah Lechtman, Sarah Lechtman, Hugues Chabriat, Hugues Chabriat, Hugues Chabriat, Eric Jouvent, Eric Jouvent, Eric Jouvent, Stéphanie Guey, Stéphanie Guey, Stéphanie Guey

Format: Article
Diterbitkan: Frontiers Media S.A. 2019-09-01

Deskripsi

Cerebral amyloid angiopathy related inflammation (CAA-RI) is a rare form of CAA characterized by subacute encephalitic symptoms (cognitive decline, seizures, focal deficits) associated with extensive and confluent white matter lesions co-localizing with lobar microbleeds on brain MRI. We report two cases of unusual CAA-RI mimicking meningoencephalitis but without typical brain lesions on FLAIR and T2* sequences. These 2 cases may extend the clinical spectrum of CAA-RI by suggesting the possible occurrence of quite purely meningeal forms of CAA-RI.