Multimodality Imaging of Fabry Disease Cardiomyopathy Complicated With Coronary Vasospasm
oleh: Tomohiro Tahara, MD, Eisuke Usui, MD, PhD, Masahiro Hada, MD, PhD, Hiroki Ueno, MD, Tsunekazu Kakuta, MD, PhD
| Format: | Article |
|---|---|
| Diterbitkan: | Elsevier 2024-04-01 |
Deskripsi
A 41-year-old man with resting angina was diagnosed with a coronary vasospasm and subsequently with Fabry disease exhibiting low serum α-galactosidase A activity. High computed tomography (CT)–derived extracellular volume was detected in the apical inferior wall of the left ventricle suggesting myocardial fibrosis, potentially from vasospasm-related ischemia and/or microvascular dysfunction.