VEXAS syndrome as a cause for multifocal, relapsing head and neck inflammation

oleh: Aoife Heeney, Rachael Wu, Conall Fitzgerald, Nina Orfali, Nadim Akasheh, Conor Magee

Format: Article
Diterbitkan: Wiley 2024-07-01

Deskripsi

Key Clinical Message VEXAS syndrome (vacuoles, E1 enzyme, X‐linked, autoinflammatory, somatic) is a novel autoinflammatory syndrome. We describe a case of VEXAS syndrome with upper airway and oral cavity involvement which are not well described in the literature.