Orthotropic liver transplantation for intractable neurological manifestations of Wilson′s disease
oleh: Vaibhav K Sutariya, Anad H Tank, Pranjal R Modi
| Format: | Article |
|---|---|
| Diterbitkan: | Wolters Kluwer Medknow Publications 2015-01-01 |
Deskripsi
Wilson′s disease (WD) is an inherited autosomal recessive disorder characterized by copper accumulation and toxicity, affecting mainly the liver and brain. Orthotopic liver transplantation (OLT) is the definitive therapy for patients with WD. Acute fulminant hepatic failure and decompensated cirrhosis are well-established indications for OLT. Patients with severe neurologic impairment can also be benefited by OLT. Here, we present a patient who underwent OLT for isolated neurological WD.