Pulsatile enophthalmos, severe esotropia, kinked optic nerve and visual loss in neurofibromatosis type-1

oleh: Virender Sachdeva, Nazmul Haque, Avinash Pathengay, Ramesh Kekunnaya

Format: Article
Diterbitkan: Wolters Kluwer Medknow Publications 2015-01-01

Deskripsi

Neurofibromatosis Type I if associated with aplasia of greater wing of sphenoid may be associated with a pulsatile exophthalmos. However, very rarely it may be associated with a pulsatile enophthalmos. This clinical image describes a rare presentation with pulsatile enophthalmos, esotropia and kinking of the optic nerve due to neurofibomatosis type I.