The Report of a Very Rare Case of Peseudoxanthomatous Mastocytosis

oleh: Mahmoud Farshchain, Abbas Zamanian, Alireza Monsef

Format: Article
Diterbitkan: Hamadan University of Medical Sciences 2001-06-01

Deskripsi

Diffuse cutaneous mastocytosis is very rare variety mast-cell disorder    which is called peseudoxanthomatous mastocytosis. Our case was a man    who was eighteen years old. He suffered from yellow papules on the neck,    extremities , axillary and groins. The appearance of large blisters following    mild trauma or occuring spontaneously. Our patients Pruritus was not very    server.          The examination of his skin revealed yellow boggy and thickened skin    with a doughy consistency without systemic involvement. Considering    the clinical signs and using the skin biopsy reports of the patient, the    illness was diagnosed as peseudoxanthomatous mastocytosis.