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Bullous Ichthyosiform Erythroderma With Unusual Presentation
oleh: Ghosh Arghyaprasun, Dey Sunil Kumar, Mandal Kakali, Kundu Mousumi
Format: | Article |
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Diterbitkan: | Wolters Kluwer Medknow Publications 2003-01-01 |
Deskripsi
Bullous ichthyosiform erythroderma is a rare autosomal dominant disorder of keratinization resulting in increased epidermal cell transit time. We describe a teenager who had five members of his family similarly affected with sparing of face, neck and upper part of chest.