Bullous Ichthyosiform Erythroderma With Unusual Presentation

oleh: Ghosh Arghyaprasun, Dey Sunil Kumar, Mandal Kakali, Kundu Mousumi

Format: Article
Diterbitkan: Wolters Kluwer Medknow Publications 2003-01-01

Deskripsi

Bullous ichthyosiform erythroderma is a rare autosomal dominant disorder of keratinization resulting in increased epidermal cell transit time. We describe a teenager who had five members of his family similarly affected with sparing of face, neck and upper part of chest.