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Large aortic aneurysm and dissection in a patient with Marfan's syndrome
oleh: Fernando Pivatto Júnior, Leila Denise Cardoso Ramos, Murilo Foppa, Felipe Soares Torres
Format: | Article |
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Diterbitkan: | Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) 2015-04-01 |
Deskripsi
Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.