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<p>Cystic fibrosis (CF) is the most common autosomal recessive lethal hereditary disorder among whites. Survival of patients with CF has progressively improved over the last four decades.</p><p>As life expectancy has been greatly extended, complications like osteopenia and CF-related diabetes mellitus (CFRDM) occur. In our article, a new management of these two complications is described.</p><p>Gastrointestinal tract, exocrine pancreas and liver are also affected in CF.</p><p>Maintaining good nutrition while treating pancreatic insufficiency, treating gastroesophageal reflux disease and treating liver disease are very important issues in the treatment gastrointestinal tract disease in CF.</p><p>As the CF patient population median survival increases,  a growing number of adolescents require care in the adult health care system which must be capable of responding appropriately to their needs.</p><p>We present a model of transition from paediatric to adult medical care in our CF center.</p>