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Apparently isolated CNS involvement in Erdheim-Chester disease: Case report
oleh: Giuseppe Romano, Mario Cirillo, Simona Bonavita, Giuseppe Toro, Andrea Di Pietro, Luigi Lavorgna, Elisabetta Maida, Francesca Pagliuca, Fabrizio Urraro, Cinzia Coppola, Giacomo Lus, Elisabetta Signoriello
Format: | Article |
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Diterbitkan: | Elsevier 2023-12-01 |
Deskripsi
We present the case of a 48-year-old-woman with apparently isolated central nervous system Erdheim-Chester disease characterized by brainstem involvement. Erdheim-Chester disease is extremely rare and multisystem impairment should always be sought in the suspicion of such pathology.