Apparently isolated CNS involvement in Erdheim-Chester disease: Case report

oleh: Giuseppe Romano, Mario Cirillo, Simona Bonavita, Giuseppe Toro, Andrea Di Pietro, Luigi Lavorgna, Elisabetta Maida, Francesca Pagliuca, Fabrizio Urraro, Cinzia Coppola, Giacomo Lus, Elisabetta Signoriello

Format: Article
Diterbitkan: Elsevier 2023-12-01

Deskripsi

We present the case of a 48-year-old-woman with apparently isolated central nervous system Erdheim-Chester disease characterized by brainstem involvement. Erdheim-Chester disease is extremely rare and multisystem impairment should always be sought in the suspicion of such pathology.