Heart failure with multiple cardiac masses: Extensive cardiac involvement in Rosai–Dorfman disease

oleh: Gopal Chandra Ghosh, Grace Rebecca, Elizabeth Joseph, George Joseph

Format: Article
Diterbitkan: Elsevier 2018-01-01

Deskripsi

Rosai–Dorfman disease (RDD) is a non-malignant disease. Pathologically it is characterised by histiocytic proliferation. A typical clinical presentation is painless generalised lymphadenopathy. Extra nodal involvement can be seen in 20–40% of cases. Cardiac involvement is rare and suggests a poor prognosis. We report a case of RDD with extensive cardiac involvement, initially masquerading as multiple cardiac thrombi in the background of underlying antiphospholipid antibody syndrome.