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Heart failure with multiple cardiac masses: Extensive cardiac involvement in Rosai–Dorfman disease
oleh: Gopal Chandra Ghosh, Grace Rebecca, Elizabeth Joseph, George Joseph
Format: | Article |
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Diterbitkan: | Elsevier 2018-01-01 |
Deskripsi
Rosai–Dorfman disease (RDD) is a non-malignant disease. Pathologically it is characterised by histiocytic proliferation. A typical clinical presentation is painless generalised lymphadenopathy. Extra nodal involvement can be seen in 20–40% of cases. Cardiac involvement is rare and suggests a poor prognosis. We report a case of RDD with extensive cardiac involvement, initially masquerading as multiple cardiac thrombi in the background of underlying antiphospholipid antibody syndrome.