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Extraosseous Ewing′s sarcoma / primitive neuroectodermal tumor of the sacral nerve plexus
oleh: MK Narula, Nishant Gupta, Rama Anand, Sudhir Kapoor
Format: | Article |
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Diterbitkan: | Thieme Medical and Scientific Publishers Pvt. Ltd. 2009-04-01 |
Deskripsi
We report an unusual case of Ewing′s sarcoma / primitive neuroectodermal tumor (PNET) of the sacral nerve plexus in a 9-year-old boy who presented with a soft tissue swelling and severe piercing pain in the lower back region. MRI of the lumbosacral spine showed a lobulated soft tissue mass with clubbed finger-like projections along the path of the sacral nerves, which had caused widening of the spinal canal and the sacral foramina (S2-S4 level). There was presacral extension and posterior scalloping of the sacral vertebrae. Histopathology of the lesion confirmed Ewing′s sarcoma / PNET of the sacral spinal nerve plexus. The patient responded favorably to chemotherapy and radiotherapy, showing clinical and radiological improvement.