Incomplete Shone’s Complex with BAV and VSD in Adult Diagnosed by Echocardiography

oleh: Yichen Qu, MD, Ya Yang, MD, Jinjie Xie, MD, Rongjuan Li, MD, Han Zhang, MD, Li Song, MD, Yueli Wang, MD, Jing Li, MD

Format: Article
Diterbitkan: Editorial Office of Advanced Ultrasound in Diagnosis and Therapy 2021-06-01

Deskripsi

Abstract: The Shone’s complex, defined as a constellation of parachute mitral valve (PMV), supravalvular ring of the left atrium, subaortic stenosis, and aorta coarctation, is a rare entity, which more commonly occurs in its incomplete form. We report the case of a 28-year-old female patient who presented for chest congestion and palpitation with history of congenital mitral valve malformation. Echocardiography revealed the coexistence of PMV, aortic coarctation with bicuspid aortic valve (BAV), and ventricular septum defect (VSD). The patient then received surgical intervention. The diagnosis of Shone’s complex with BAV and VSD made by echocardiography were confirmed later at surgery.