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Defective dystrophic thymus determines degenerative changes in skeletal muscle
oleh: Andrea Farini, Clementina Sitzia, Chiara Villa, Barbara Cassani, Luana Tripodi, Mariella Legato, Marzia Belicchi, Pamela Bella, Caterina Lonati, Stefano Gatti, Massimiliano Cerletti, Yvan Torrente
Format: | Article |
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Diterbitkan: | Nature Portfolio 2021-04-01 |
Deskripsi
Immune cells are known to aggravate the inflammatory impact of Duchene muscular dystrophy. Here, the authors describe impaired thymic development and suggest thymic involution in this model of disease is linked to disease acceleration due to impaired immunological tolerance.