Hasil Pencarian - Matthias Klugmann
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Dual-function AAV gene therapy reverses late-stage Canavan disease pathology in mice oleh Dominik Fröhlich, Elizabeth Kalotay, Georg von Jonquieres, Andre Bongers, Brendan Lee, Alexandra K. Suchowerska, Gary D. Housley, Matthias Klugmann, Matthias Klugmann
Diterbitkan 2022-12-01
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The Leukodystrophies HBSL and LBSL—Correlates and Distinctions oleh Annapoorani Muthiah, Gary D. Housley, Matthias Klugmann, Dominik Fröhlich
Diterbitkan 2021-01-01
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Optogenetic release of ACh induces rhythmic bursts of perisomatic IPSCs in hippocampus. oleh Daniel A Nagode, Ai-Hui Tang, Miranda A Karson, Matthias Klugmann, Bradley E Alger
Diterbitkan 2011-01-01
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Loss of central auditory processing in a mouse model of Canavan disease. oleh Georg von Jonquieres, Kristina E Froud, Claudia B Klugmann, Ann C Y Wong, Gary D Housley, Matthias Klugmann
Diterbitkan 2014-01-01
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Semaphorin 6A improves functional recovery in conjunction with motor training after cerebral ischemia. oleh Andreas Rogalewski, Tanjew Dittgen, Matthias Klugmann, Friederike Kirsch, Carola Krüger, Claudia Pitzer, Jens Minnerup, Wolf-Rüdiger Schäbitz, Armin Schneider
Diterbitkan 2010-01-01
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Gene therapy mediated seizure suppression in Genetic Generalised Epilepsy: Neuropeptide Y overexpression in a rat model oleh Kim L. Powell, Xavier Fitzgerald, Claire Shallue, Valentina Jovanovska, Matthias Klugmann, Georg Von Jonquieres, Terence J. O'Brien, Margaret J. Morris
Diterbitkan 2018-05-01
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Aspartoacylase-lacZ knockin mice: an engineered model of Canavan disease. oleh Nadine Mersmann, Dmitri Tkachev, Ruth Jelinek, Philipp Thomas Röth, Wiebke Möbius, Torben Ruhwedel, Sabine Rühle, Wolfgang Weber-Fahr, Alexander Sartorius, Matthias Klugmann
Diterbitkan 2011-01-01
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Expression Pattern of the Aspartyl-tRNA Synthetase DARS in the Human Brain oleh Dominik Fröhlich, Alexandra K. Suchowerska, Carola Voss, Ruojie He, Ruojie He, Ernst Wolvetang, Georg von Jonquieres, Cas Simons, Thomas Fath, Gary D. Housley, Matthias Klugmann
Diterbitkan 2018-03-01
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A Hypomorphic Dars1D367Y Model Recapitulates Key Aspects of the Leukodystrophy HBSL oleh Dominik Fröhlich, Marisa I. Mendes, Andrew J. Kueh, Andrew J. Kueh, Andre Bongers, Marco J. Herold, Marco J. Herold, Gajja S. Salomons, Gary D. Housley, Matthias Klugmann
Diterbitkan 2021-01-01
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Glial promoter selectivity following AAV-delivery to the immature brain. oleh Georg von Jonquieres, Nadine Mersmann, Claudia Bettina Klugmann, Anne Editha Harasta, Beat Lutz, Orla Teahan, Gary David Housley, Dominik Fröhlich, Eva-Maria Krämer-Albers, Matthias Klugmann
Diterbitkan 2013-01-01
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In vivo characterization of the aspartyl-tRNA synthetase DARS: Homing in on the leukodystrophy HBSL oleh Dominik Fröhlich, Alexandra K. Suchowerska, Ziggy H.T. Spencer, Georg von Jonquieres, Claudia B. Klugmann, Andre Bongers, Fabien Delerue, Holly Stefen, Lars M. Ittner, Thomas Fath, Gary D. Housley, Matthias Klugmann
Diterbitkan 2017-01-01
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Behavioral and Neurochemical Phenotyping of Mice Incapable of Homer1a Induction oleh Michael C. Datko, Jia-Hua Hu, Melanie Williams, Cindy M. Reyes, Kevin D. Lominac, Georg von Jonquieres, Matthias Klugmann, Paul F. Worley, Karen K. Szumlinski, Karen K. Szumlinski, Karen K. Szumlinski
Diterbitkan 2017-11-01
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Neurotransmitter-triggered transfer of exosomes mediates oligodendrocyte-neuron communication. oleh Carsten Frühbeis, Dominik Fröhlich, Wen Ping Kuo, Jesa Amphornrat, Sebastian Thilemann, Aiman S Saab, Frank Kirchhoff, Wiebke Möbius, Sandra Goebbels, Klaus-Armin Nave, Anja Schneider, Mikael Simons, Matthias Klugmann, Jacqueline Trotter, Eva-Maria Krämer-Albers
Diterbitkan 2013-07-01
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Riboswitch-controlled IL-12 gene therapy reduces hepatocellular cancer in mice oleh Matthias J. Düchs, Ramona F. Kratzer, Pablo Vieyra-Garcia, Benjamin Strobel, Tanja Schönberger, Peter Groß, Ghaith Aljayyoussi, Aradhana Gupta, Isabel Lang, Holger Klein, Sandra Martinez Morilla, Stefan Hopf, John Park, Sebastian Kreuz, Matthias Klugmann, Frederik H. Igney
Diterbitkan 2024-03-01
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AAV9-mediated gene delivery of MCT1 to oligodendrocytes does not provide a therapeutic benefit in a mouse model of ALS oleh Caroline Eykens, Elisabeth Rossaert, Sandra Duqué, Laura Rué, André Bento-Abreu, Nicole Hersmus, Annette Lenaerts, Axelle Kerstens, Nikky Corthout, Sebastian Munck, Philip Van Damme, Matthew G. Holt, Georg von Jonquires, Matthias Klugmann, Ludo Van Den Bosch, Wim Robberecht
Diterbitkan 2021-03-01
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