Hasil Pencarian - Manuela Bozzi
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Molecular Mechanisms Underlying Muscle Wasting in Huntington’s Disease oleh Manuela Bozzi, Francesca Sciandra
Diterbitkan 2020-11-01Dapatkan teks lengkap
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From adhesion complex to signaling hub: the dual role of dystroglycan oleh Francesca Sciandra, Manuela Bozzi, Manuela Bozzi, Maria Giulia Bigotti, Maria Giulia Bigotti
Diterbitkan 2023-12-01Dapatkan teks lengkap
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Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Lin... oleh Francesca Sciandra, Patrizia Bottoni, Marinella De Leo, Alessandra Braca, Andrea Brancaccio, Manuela Bozzi
Diterbitkan 2023-10-01Dapatkan teks lengkap
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Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. oleh Davide Pirolli, Francesca Sciandra, Manuela Bozzi, Bruno Giardina, Andrea Brancaccio, Maria Cristina De Rosa
Diterbitkan 2014-01-01Dapatkan teks lengkap
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The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of α-dystroglycan. oleh Sonia Covaceuszach, Manuela Bozzi, Maria Giulia Bigotti, Francesca Sciandra, Petr V Konarev, Andrea Brancaccio, Alberto Cassetta
Diterbitkan 2017-01-01Dapatkan teks lengkap
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The missense mutation C667F in murine β-dystroglycan causes embryonic lethality, myopathy and blood-brain barrier destabilization oleh Rui Lois Tan, Francesca Sciandra, Wolfgang Hübner, Manuela Bozzi, Jens Reimann, Susanne Schoch, Andrea Brancaccio, Sandra Blaess
Diterbitkan 2024-06-01Dapatkan teks lengkap
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The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy. oleh Manuela Bozzi, Alberto Cassetta, Sonia Covaceuszach, Maria Giulia Bigotti, Saskia Bannister, Wolfgang Hübner, Francesca Sciandra, Doriano Lamba, Andrea Brancaccio
Diterbitkan 2015-01-01Dapatkan teks lengkap
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Proteasome Activity Is Affected by Fluctuations in Insulin-Degrading Enzyme Distribution. oleh Diego Sbardella, Grazia Raffaella Tundo, Francesca Sciandra, Manuela Bozzi, Magda Gioia, Chiara Ciaccio, Umberto Tarantino, Andrea Brancaccio, Massimo Coletta, Stefano Marini
Diterbitkan 2015-01-01Dapatkan teks lengkap
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Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene oleh Francesca Sciandra, Bianca Maria Scicchitano, Giulia Signorino, Maria Giulia Bigotti, Barbara Tavazzi, Francesca Lombardi, Manuela Bozzi, Gigliola Sica, Bruno Giardina, Sandra Blaess, Andrea Brancaccio
Diterbitkan 2017-11-01Dapatkan teks lengkap
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The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. oleh Magda Gioia, Giovanni Francesco Fasciglione, Diego Sbardella, Francesca Sciandra, MariaLuisa Casella, Serena Camerini, Marco Crescenzi, Alessandro Gori, Umberto Tarantino, Paola Cozza, Andrea Brancaccio, Massimo Coletta, Manuela Bozzi
Diterbitkan 2018-01-01Dapatkan teks lengkap
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