Hasil Pencarian - Frances M. Platt

Perbaiki Hasil
  1. 1
    Unexpected differences in the pharmacokinetics of N-acetyl-DL-leucine enantiomers after oral dosing and their clinical relevance.

    Unexpected differences in the pharmacokinetics of N-acetyl-DL-leucine enantiomers after oral dosing and their clinical relevance. oleh Grant C Churchill, Michael Strupp, Antony Galione, Frances M Platt

    Diterbitkan 2020-01-01
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  2. 2
    Differential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C [version 1; referees: 2 approved, 1 not approved]

    Differential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C [version 1; referees: 2 approved, 1 not approved] oleh Elena-Raluca Nicoli, David Smith, Lauren Morris, Frances M. Platt

    Diterbitkan 2017-08-01
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  3. 3
    Differential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C [version 2; referees: 2 approved, 1 not approved]

    Differential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C [version 2; referees: 2 approved, 1 not approved] oleh Elena-Raluca Nicoli, Mylene Huebecker, David Smith, Lauren Morris, Frances M. Platt

    Diterbitkan 2018-04-01
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  4. 4
    Beneficial effects of anti-inflammatory therapy in a mouse model of Niemann-Pick disease type C1

    Beneficial effects of anti-inflammatory therapy in a mouse model of Niemann-Pick disease type C1 oleh David Smith, Kerri-Lee Wallom, Ian M. Williams, Mylvaganam Jeyakumar, Frances M. Platt

    Diterbitkan 2009-11-01
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  5. 5
    Critical role of iron in the pathogenesis of the murine gangliosidoses

    Critical role of iron in the pathogenesis of the murine gangliosidoses oleh Mylvaganam Jeyakumar, Ian Williams, David A. Smith, Timothy M. Cox, Frances M. Platt

    Diterbitkan 2009-06-01
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  6. 6
    Metabolomic Studies of Lipid Storage Disorders, with Special Reference to Niemann-Pick Type C Disease: A Critical Review with Future Perspectives

    Metabolomic Studies of Lipid Storage Disorders, with Special Reference to Niemann-Pick Type C Disease: A Critical Review with Future Perspectives oleh Benita Claire Percival, Miles Gibson, Philippe B. Wilson, Frances M. Platt, Martin Grootveld

    Diterbitkan 2020-04-01
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  7. 7
    Case Report: Ursodeoxycholic acid treatment in Niemann-Pick disease type C; clinical experience in four cases [version 1; referees: 2 approved]

    Case Report: Ursodeoxycholic acid treatment in Niemann-Pick disease type C; clinical experience in four cases [version 1; referees: 2 approved] oleh William R.H. Evans, Elena-Raluca Nicoli, Raymond Y. Wang, Nina Movsesyan, Frances M. Platt

    Diterbitkan 2017-08-01
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  8. 8
    Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice

    Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice oleh Brett Garner, David A. Priestman, Roland Stocker, David J. Harvey, Terry D. Butters, Frances M. Platt

    Diterbitkan 2002-02-01
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  9. 9
    Early glial activation, synaptic changes and axonal pathology in the thalamocortical system of Niemann–Pick type C1 mice

    Early glial activation, synaptic changes and axonal pathology in the thalamocortical system of Niemann–Pick type C1 mice oleh Sarah N.R. Pressey, David A. Smith, Andrew M.S. Wong, Frances M. Platt, Jonathan D. Cooper

    Diterbitkan 2012-03-01
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  10. 10
    Improved neuroprotection using miglustat, curcumin and ibuprofen as a triple combination therapy in Niemann–Pick disease type C1 mice

    Improved neuroprotection using miglustat, curcumin and ibuprofen as a triple combination therapy in Niemann–Pick disease type C1 mice oleh Ian M. Williams, Kerri-Lee Wallom, David A. Smith, Nada Al Eisa, Claire Smith, Frances M. Platt

    Diterbitkan 2014-07-01
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  11. 11
    Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease

    Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease oleh Ulrika Andersson, David Smith, Mylvaganam Jeyakumar, Terry D Butters, Mario Cortina Borja, Raymond A Dwek, Frances M Platt

    Diterbitkan 2004-08-01
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  12. 12
    Intracellular sphingosine releases calcium from lysosomes

    Intracellular sphingosine releases calcium from lysosomes oleh Doris Höglinger, Per Haberkant, Auxiliadora Aguilera-Romero, Howard Riezman, Forbes D Porter, Frances M Platt, Antony Galione, Carsten Schultz

    Diterbitkan 2015-11-01
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  13. 13
    Inhibition of the Niemann-Pick C1 protein is a conserved feature of multiple strains of pathogenic mycobacteria

    Inhibition of the Niemann-Pick C1 protein is a conserved feature of multiple strains of pathogenic mycobacteria oleh Yuzhe Weng, Dawn Shepherd, Yi Liu, Nitya Krishnan, Brian D. Robertson, Nick Platt, Gerald Larrouy-Maumus, Frances M. Platt

    Diterbitkan 2022-09-01
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  14. 14
    Acetylation turns leucine into a drug by membrane transporter switching

    Acetylation turns leucine into a drug by membrane transporter switching oleh Grant C. Churchill, Michael Strupp, Cailley Factor, Tatiana Bremova-Ertl, Mallory Factor, Marc C. Patterson, Frances M. Platt, Antony Galione

    Diterbitkan 2021-08-01
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  15. 15
    Glucosylceramide modulates membrane traffic along the endocytic pathway

    Glucosylceramide modulates membrane traffic along the endocytic pathway oleh Dan J. Sillence, Vishwajeet Puri, David L. Marks, Terry D. Butters, Raymond A. Dwek, Richard E. Pagano, Frances M. Platt

    Diterbitkan 2002-11-01
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  16. 16
    Correction to: Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease

    Correction to: Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease oleh Mylene Huebecker, Elizabeth B. Moloney, Aarnoud C. van der Spoel, David A. Priestman, Ole Isacson, Penelope J. Hallett, Frances M. Platt

    Diterbitkan 2020-01-01
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  17. 17
    Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease

    Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease oleh Mylene Huebecker, Elizabeth B. Moloney, Aarnoud C. van der Spoel, David A. Priestman, Ole Isacson, Penelope J. Hallett, Frances M. Platt

    Diterbitkan 2019-11-01
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  18. 18
    Inhibition of β-Glucocerebrosidase Activity Preserves Motor Unit Integrity in a Mouse Model of Amyotrophic Lateral Sclerosis

    Inhibition of β-Glucocerebrosidase Activity Preserves Motor Unit Integrity in a Mouse Model of Amyotrophic Lateral Sclerosis oleh Alexandre Henriques, Mylene Huebecker, Hélène Blasco, Céline Keime, Christian R. Andres, Philippe Corcia, David A. Priestman, Frances M. Platt, Michael Spedding, Jean-Philippe Loeffler

    Diterbitkan 2017-07-01
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  19. 19
    Altered Expression of Ganglioside Metabolizing Enzymes Results in GM3 Ganglioside Accumulation in Cerebellar Cells of a Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis

    Altered Expression of Ganglioside Metabolizing Enzymes Results in GM3 Ganglioside Accumulation in Cerebellar Cells of a Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis oleh Aleksandra Somogyi, Anton Petcherski, Benedikt Beckert, Mylene Huebecker, David A. Priestman, Antje Banning, Susan L. Cotman, Frances M. Platt, Mika O. Ruonala, Ritva Tikkanen

    Diterbitkan 2018-02-01
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  20. 20
    Heat shock protein amplification improves cerebellar myelination in the Npc1nih mouse modelResearch in context

    Heat shock protein amplification improves cerebellar myelination in the Npc1nih mouse modelResearch in context oleh James Gray, María E. Fernández-Suárez, Maysa Falah, David Smith, Claire Smith, Ecem Kaya, Ashley M. Palmer, Cathrine K. Fog, Thomas Kirkegaard, Frances M. Platt

    Diterbitkan 2022-12-01
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