Hasil Pencarian - Christoph S Clemen
Anda harus masuk terlebih dahulu
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Domain Organization of the UBX Domain Containing Protein 9 and Analysis of Its Interactions With the Homohexameric AAA + ATPase p97 (Valosin-Containing Protein) oleh Jana Riehl, Ramesh Rijal, Leonie Nitz, Christoph S. Clemen, Christoph S. Clemen, Christoph S. Clemen, Andreas Hofmann, Ludwig Eichinger
Diterbitkan 2021-09-01
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Lack of Desmin in Mice Causes Structural and Functional Disorders of Neuromuscular Junctions oleh Nane Eiber, Franziska Fröb, Mirjam Schowalter, Christian Thiel, Christian Thiel, Christoph S. Clemen, Christoph S. Clemen, Christoph S. Clemen, Rolf Schröder, Rolf Schröder, Said Hashemolhosseini, Said Hashemolhosseini
Diterbitkan 2020-10-01
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Immortalised murine R349P desmin knock-in myotubes exhibit a reduced proton leak and decreased ADP/ATP translocase levels in purified mitochondria oleh Carolin Berwanger, Dominic Terres, Dominik Pesta, Britta Eggers, Katrin Marcus, Ilka Wittig, Rudolf J. Wiesner, Rolf Schröder, Christoph S. Clemen
Diterbitkan 2024-06-01
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Growing Old Too Early: Skeletal Muscle Single Fiber Biomechanics in Ageing R349P Desmin Knock-in Mice Using the <i>MyoRobot</i> Technology oleh Charlotte Pollmann, Michael Haug, Barbara Reischl, Gerhard Prölß, Thorsten Pöschel, Stefan J Rupitsch, Christoph S Clemen, Rolf Schröder, Oliver Friedrich
Diterbitkan 2020-07-01
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Heteromeric p97/p97R155C complexes induce dominant negative changes in wild-type and autophagy 9-deficient Dictyostelium strains. oleh Khalid Arhzaouy, Karl-Heinz Strucksberg, Sze Man Tung, Karthikeyan Tangavelou, Maria Stumpf, Jan Faix, Rolf Schröder, Christoph S Clemen, Ludwig Eichinger
Diterbitkan 2012-01-01
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Functional Characterisation of the Autophagy ATG12~5/16 Complex in <i>Dictyostelium discoideum</i> oleh Malte Karow, Sarah Fischer, Susanne Meßling, Roman Konertz, Jana Riehl, Qiuhong Xiong, Ramesh Rijal, Prerana Wagle, Christoph S. Clemen, Ludwig Eichinger
Diterbitkan 2020-05-01
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Correction: Heteromeric p97/p97R155C Complexes Induce Dominant Negative Changes in Wild-Type and Autophagy 9-Deficient Dictyostelium strains. oleh Khalid Arhzaouy, Karl-Heinz Strucksberg, Sze Man Tung, Karthikeyan Tangavelou, Maria Stumpf, Jan Faix, Rolf Schröder, Christoph S Clemen, Ludwig Eichinger
Diterbitkan 2018-01-01
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An Intronic Heterozygous <i>SYNE2</i> Splice Site Mutation: A Rare Cause for Myalgia and hyperCKemia? oleh Theresa Paulus, Natalie Young, Emily Jessop, Carolin Berwanger, Christoph Stephan Clemen, Rolf Schröder, Rafal Ploski, Christian Hagel, Yorck Hellenbroich, Andreas Moser, Iakowos Karakesisoglou
Diterbitkan 2024-03-01
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The p97-UBXD8 complex regulates ER-Mitochondria contact sites by altering membrane lipid saturation and composition oleh Rakesh Ganji, Joao A. Paulo, Yuecheng Xi, Ian Kline, Jiang Zhu, Christoph S. Clemen, Conrad C. Weihl, John G. Purdy, Steve P. Gygi, Malavika Raman
Diterbitkan 2023-02-01
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Proteasomes of Autophagy-Deficient Cells Exhibit Alterations in Regulatory Proteins and a Marked Reduction in Activity oleh Qiuhong Xiong, Rong Feng, Sarah Fischer, Malte Karow, Maria Stumpf, Susanne Meßling, Leonie Nitz, Stefan Müller, Christoph S. Clemen, Ning Song, Ping Li, Changxin Wu, Ludwig Eichinger
Diterbitkan 2023-05-01
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Homozygous expression of the myofibrillar myopathy-associated p.W2710X filamin C variant reveals major pathomechanisms of sarcomeric lesion formation oleh Julia Schuld, Zacharias Orfanos, Frédéric Chevessier, Britta Eggers, Lorena Heil, Julian Uszkoreit, Andreas Unger, Gregor Kirfel, Peter F. M. van der Ven, Katrin Marcus, Wolfgang A. Linke, Christoph S. Clemen, Rolf Schröder, Dieter O. Fürst
Diterbitkan 2020-09-01
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Heart failure after pressure overload in autosomal-dominant desminopathies: Lessons from heterozygous DES-p.R349P knock-in mice. oleh Florian Stöckigt, Lars Eichhorn, Thomas Beiert, Vincent Knappe, Tobias Radecke, Martin Steinmetz, Georg Nickenig, Viktoriya Peeva, Alexei P Kudin, Wolfram S Kunz, Carolin Berwanger, Lisa Kamm, Dorothea Schultheis, Ursula Schlötzer-Schrehardt, Christoph S Clemen, Rolf Schröder, Jan W Schrickel
Diterbitkan 2020-01-01
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Early signs of architectural and biomechanical failure in isolated myofibers and immortalized myoblasts from desmin-mutant knock-in mice oleh Stefanie Diermeier, Julian Iberl, Kristina Vetter, Michael Haug, Charlotte Pollmann, Barbara Reischl, Andreas Buttgereit, Sebastian Schürmann, Marina Spörrer, Wolfgang H. Goldmann, Ben Fabry, Fatiha Elhamine, Robert Stehle, Gabriele Pfitzer, Lilli Winter, Christoph S. Clemen, Harald Herrmann, Rolf Schröder, Oliver Friedrich
Diterbitkan 2017-05-01
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VCP suppresses proteopathic seeding in neurons oleh Jiang Zhu, Sara Pittman, Dhruva Dhavale, Rachel French, Jessica N. Patterson, Mohamed Salman Kaleelurrrahuman, Yuanzi Sun, Jaime Vaquer-Alicea, Gianna Maggiore, Christoph S. Clemen, William J. Buscher, Jan Bieschke, Paul Kotzbauer, Yuna Ayala, Marc I. Diamond, Albert A. Davis, Conrad Weihl
Diterbitkan 2022-04-01
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Desmin Knock-Out Cardiomyopathy: A Heart on the Verge of Metabolic Crisis oleh Barbara Elsnicova, Daniela Hornikova, Veronika Tibenska, David Kolar, Tereza Tlapakova, Benjamin Schmid, Markus Mallek, Britta Eggers, Ursula Schlötzer-Schrehardt, Viktoriya Peeva, Carolin Berwanger, Bettina Eberhard, Hacer Durmuş, Dorothea Schultheis, Christian Holtzhausen, Karin Schork, Katrin Marcus, Jens Jordan, Thomas Lücke, Peter F. M. van der Ven, Rolf Schröder, Christoph S. Clemen, Jitka M. Zurmanova
Diterbitkan 2022-10-01
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